pgaiims-Fort-Worth-Star-Telegram

Q: Ductus dependent blood flow is required for all of these congenital heart diseases except:

(a) Persistent truncus arteriosus
(b) Hypoplastic left heart syndrome
(c) Pulmonary stenosis
(d) TGA with intact septum.


                                                                                                   A: a. Persistent....

Q: A child is admitted on 7th day of life with severe respiratory distress and shock. He was discharged 2 days back healthy. What could be the probable diagnosis:

(a) Large VSD
(b) Hypoplastic left heart syndrome
(c) Ebstein anomaly
(d) AP window defect.



                                                                                                   A: b. Hypoplastic...

Q: International prognostic index for lymphomas includes the following prognostic factors except:

(a) Stage of disease
(b) No: of extralymphatic sites involved
(c) LDH
(d) Hemoglobin and albumin


                                                                                                   A: d. Hemoglobin...

Q: A study under Australian collaborative trial on steroid use in neonates showed:

(a) No difference between placebo and steroid
(b) Steroids to children cause behavioural worsening
(c) Steroids to children cause reduction in head circumference
(d) Steroids to children cause neurosensitivity degradation.



                                                                                                   A: b. behavioural...

Q: In a child with respiratory distress, failure to thrive, the sweat chloride levels were estimated to be 35 meq/l and 41 meq/l. What is the next best to do:

(a) Nasal transmembrane potential difference
(b) DNA analysis of F 508 mutation
(c) CT chest
(d) 72 hour fecal fat estimation.


                                                                                                   A: a. Nasal .....

Q: Hypoplasia of limbs and scarring is due to:

(a) Varicella
(b) Herpes simplex
(c) Rubella
(d) Toxoplasmosis.



                                                                                                   A: a. Varicella....

Q: A pregnant lady had no complaints but mild cervical lymphadenopathy in first trimester. She was prescribed spiramycin, but she was non-compliant. Baby was born with hydrocephalus and intracerebral calcification. Which of these is a likely cause:

(a) Rubella
(b) Toxoplasmosis
(c) CMV
(d) Herpes.


                                                                                                   A: Toxoplasmosis

Q: A 3.5 male infant born at term after an uncomplicated pregnancy and delivery develops respiratory distress shortly after birth and requires mechanical ventilation. The chest radiograph reveals a normal cardiothymic silhouette but a diffuse ground glass appearance to the lung fields. Surfactant replacement fails to improve gas exchange. Over the first week of life, the hypoxemia worsens. Results of routine culture and echocardiographic findings are negative. A term female sibling died at 1 month of age with respiratory distress. Which of the following is the most likely diagnosis:

(a) TAPVC
(b) Meconium aspiration
(c) Neonatal pulmonary alveolar proteinosis
(d) Disseminated herpes simplex infection.



                                                                                                   A: c. Neonatal....

Q: A 4 week old female child with normal genitalia presents to the emergency department with severe dehydration, hyperkalemia and hyponatremia. The measurement of blood levels of which of the following will be helpful:

(a) 17 hydroxy progesterone
(b) Renin
(c) Cortisol
(d) Aldosterone.


                                                                                                   A: d. Aldosterone

Q: Which of the following is not a feature of juvenile idiopathic arthritis:

(a) Rheumatoid arthritis
(b) Spikes of high fever
(c) Uveitis
(d) Raynaud's phenomenon.



                                                                                                   A: d. Raynaud's...

Q: A 5-yr old boy presents with pubic hair development. He is tall and has increased pigmentation of his genitalia and phallic enlargement. Blood pressure is 130/90 mm of Hg. Measurement of which of the following hormones would most likely be diagnostic:

(a) Increased 17 beta hydroxy progesterone
(b) Increased cortisol
(c) Increased aldosterone
(d) Increased 11 deoxy cortisol.


                                                                                                   A: d. Increased 11...

Q: A 2 month old infant is presented with failure to thrive, recurrent emesis, hepatosplenomegaly and adrenal insufficiency. Adrenal calcification is noted radiologically. The most likely diagnosis is:

(a) Adrenal hemorrhage
(b) Wolman's disease
(c) Pheochromocytoma
(d) Addison's disease.


                                                                                                   A: b. Wolman's ....

Q: All of the following statements about congenital rubella are true except:

(a) IgG persists for more than 6 months
(b) IgM antibody is present at birth
(c) Most common anomalies are hearing and birth defects
(d) Increased risk of congenital malformation if infection occurs after 16 weeks.



                                                                                                   A: d. Increased....

Q:  A previously healthy 6 week old female infant is found unresponsive in her crib. In the emergency department, she is noted to be well developed and well nourished with normal blood pressure and appearance of the genitalia, but with increased pigmentation of her skin. Blood glucose level is 30 mg/dl. The most likely diagnosis is:

(a) CAH due to 21 hydroxylase deficiency
(b) Familial glucocorticoid deficiency
(c) Cushing syndrome
(d) Insulinoma.


                                                                                                   A: b. Familial gluco..

Q: A child comes with steroid resistant nephrotic syndrome secondary to FSGS, not responsive to methylprednisolone. what next should be given:

(a) Oral cyclophosphamide
(b) Oral cyclosporine
(c) Oral mycophenolate
(d) IV cyclophosphamide.


                                                                                                   A: b. Oral cyclospo..

Q: Which of the following about cystic fibrosis is not true:

(a) Autosomal recessive
(b) Abnormality in CFTR which leads to defective calcium transport
(c) Mutation in cystic fibrosis transport regulator
(d) Decrease in ENaC activity.



                                                                                                   A: b. Abnormality...

Q: Most common organism associated with cystic fibrosis:

(a) Pseudomonas aeuroginosa
(b) Burkholderia cepacia
(c) Pleisomonas
(d) Aeromonas.



                                                                                                   A: a. Pseudo....

Q: A male child with Fanconi syndrome with nephrocalcinosis has a variant of Dent's disease. All are true except:

(a) Hypercalciuria
(b) Proteinuria
(c) Similar presentation in father
(d) Rickets.


                                                                                                   A: c. Similar....